Nasal gliomas are rare, benign, congenital tumors that are thought to be the result of an error in embryogenic development. The origin of this tumor is thought the same type as encephaloceles, but other hypotheses had been also proposed. They are 60% extransal and 30% intranasal and the rest are mainly combined defect. In 20% of the cases, there is a mainly fibrous connection to the intracranial space, but meningeal continuity is not found. Since the first reported case was made by Reid in 1852, and the term of nasal glioma was first used in 1900 by Schmidt, about 140 cases have been reported. Recently we experienced a case of nasal glioma in a 3 years old male patient who had a slow growing plpable mass on right epicanthal region since early infancy. The physical and radiological examinations were within normal limits. Surgical excision was made. During the operarion, any connection to the cranial space was not found. Crossly, it revealed several fragmented light yellow and firm masses, measuring up to 3.0×2.5×2.0cm, and showed also light yellow and slightly trabeculated cut surface. Microscopically, it was composed of fibrillary astrocytes interlaced with fibrous connective tissue with focally microcystic change.