Pulmonary arteriovenous fistula (PAVF) is abnormally dilated vessels that provide a right-to-left shunt between pulmonary artery and pulmonary vein and is clinically divided into simple and complex type. Here, we report four cases of surgically resected sporadic PAVFs presenting various clinical and histologic spectrums. Cases 1 (a 57-old-female) and 2 (a 54-old-female) presented as incidentally identified single aneurysmal fistulas and the lesions were surgically removed without complication. On the other hand, case 3 (an 11-old-male) showed diffuse dilated vascular sacs involving both lungs and caused severe hemodynamic and pulmonary dysfunction. Embolization and surgical resection of the main lesion failed to relieve the symptoms. Case 4 (a 36-old-male) had a localized multiloculated cyst clinically mimicking congenital cystic adenomatoid malformation. Microscopically, the lesion consisted of dilated thick vessels, consistent with the diagnosis of fistulous arteriovenous malformation/hemangioma.
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The Shunt of It Brittany M. Scarpato, Jamie McDonald, Pinar Bayrak-Toydemir, C. Gregory Elliott, Barbara C. Cahill, Lyska L. Emerson, Lynn M. Keenan Chest.2023; 163(5): e201. CrossRef
Pyogenic Brain Abscesses in a Patient With Digital Clubbing Vimal Kumar Paliwal, Sucharita Anand, Vivek Singh JAMA Neurology.2020; 77(1): 129. CrossRef
Recurrent hemoptysis caused by arteriovenous malformation Ivana Meta-Jevtović, Romana Suša, Bojan Đokić Medicinski casopis.2020; 54(3): 120. CrossRef
A 10-year-old boy with dyspnea and hypoxia: abernathy malformation masquerading as pulmonary arteriovenous fistula Lijian Xie, Yun Li, Xunwei Jiang, Jian Zhao, Tingting Xiao BMC Pediatrics.2019;[Epub] CrossRef
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