Endometriosis is a tumorous condition composed of endometrial tissue, either progressing into the uterine wall from the endometrium itself(adenomyosis) or found outside the uterus(endometriosis) usually in the pelvic organ, on the pelvic peritoneum, or in the retroperitoneal tissue. Endometriosis involving the ureter is an uncommon disease and has been reported sporadically since Cullen(1917) first reported a case of bilateral involvement of the ureter. In a recent review of literature, there have been below than 90 cases of endometriosis of the ureter recorded. Authors have experienced a case of endometriosis of the ureter with adenomyosis in a 49-year-old multiparous woman who complained of intermittent gross hematuria for one year. On physical examination, a palpable mass was noted at pelvic portion. IVP and RGP findings showed a hydronephrosis with ureteral stricture on distal portion of the right ureter. Under the impression of the uterine myoma and right ureteral stricture, total abdominal hysterectomy, right salpingo-oophorectomy and uretero-ureterostomy were performed.