A case primary carcinoma of the pancreas in a 4 years o14 Korean male is presented. A large mass, 11×9×8, in the tail with direct invasion to the splenic parenchyma and metastasis to the regional surgery, the patient developed liver metastasis 15 month later and eventually death ensued at 22 months postoperatively. Despite the radical surgery, the patient developed liver metastasis 15 months later and eventually death ensured at 22 months postoperatively. On light microscopic examination, most areas simulated an well differentiated acinar carcinoma with occasional foci of islet like configuration and squamous metaplasia. This was supported by electron microscopy which revealed zymogen granules of acinar cells in the tumor cells. These features, common to other reported cases in one way or the other, have been suggested as a peculiarity of childhood pancreatic carcinoma. Carcinoma of the pancreas, infantile type, is one of the very rare malignant tumor and less than 50 cases are reported in English literatures. To our knowledge this probable is the first reported case in Korea.