Abstract

Two 11 year and 14 year old girls presented with urinary incontinence form birth. In the former, IVP and renogram revealed adult thumb tip sized left kidney located at L2～3 level. Cystoscopically ureteral olifice of left side was not identified and ureteral orifice like fold was observed at 12 o'clock direction by vaginoscopy. The latter, right kidney was not visualized in IVP. After nephrectomized incontinence was disappeared and they discharged without any complication. The removed kidneys weighed 3.8g and 2.7gm respectively, and pathologic diagnosis of both was segmental dysplsia. A brief review of literature is added.