1 |
M |
10 |
LFT abnormality, hepatosplenomeg-aly, multiple enlarged lymph node (posterior neck, axilla and inguinal area) mosquito-bite hypersentivity |
2YA |
LN, BM |
Absent |
Peripheral T-cell lymphoma |
77.6 (initial), 71.24-2,936 |
Positive |
EB-VCA, IgG(+) |
CD3+ |
Monoclonal/monomorphic |
106B |
10 mo |
Dead |
EB-VCA, IgM(–) |
EBV-EA(+) |
EBNA(+) |
2 |
F |
14 |
Fever, sore throat, IgA nephropathy, hydroa vacciniforme |
Infancy |
Skin, BM |
Absent |
T/NKcell lymphoma |
NA |
NA |
NA |
CD3+ |
NA |
CHOP, ESHAP |
18 mo |
Dead |
3 |
M |
15 |
Nausea, weight loss, LFT abnormality, Herpes zoster infection |
2MA |
Liver, BM |
Present |
None |
258.5 (initial), 22-258.5 |
Positive |
EB-VCA, IgG(+) |
CD3+ |
Monoclonal/monomorphic |
HLH-2004a
|
7 mo |
Dead |
EB-VCA, IgM(–) |
CD4>CD8 |
EBV-EA(±) |
CD56– |
EBNA(+) |
|
4 |
M |
15 |
Mosquito-bite hypersensitivity, palpable neck mass, NK lymphocytosis |
2WA |
LN,BM |
Absent |
None |
529.8 (initial), 40-529.8 |
Positive |
EB-VCA, IgG(+) |
CD3+ |
NA |
ABVD |
45 mo |
Alive |
EB-VCA, IgM(–) |
CD4+ |
EBV-EA(+) |
CD8+ |
EBNA(+) |
CD56– |
5 |
M |
16 |
Fever and skin lesion (4YA), bowel perforation (7YA) mosquito-bite hypersensitivity, NK lymphocytosis |
Infancy |
Skin, BM |
Present |
None |
2,290 (initial), 7-2,290 |
Positive |
EB-VCA, IgG(+) |
CD3+ |
Polyclonal/polymorphic |
HLH-2004a
|
46 mo |
Alive |
EB-VCA, IgM(–) |
CD4+ |
EBV-EA(+) |
CD8+ |
EBNA(+) |
CD56– |
6 |
M |
21 |
Mosquito-bite hypersensitivity, fever, epigastric pain, nausea, NK lymphocytosis |
7MA |
Liver, BM |
Present |
None |
NA |
NA |
EB-VCA, IgG(+) |
NC |
NA |
IMVP-16PD |
3 mo |
Dead |
EB-VCA, IgM(–) |
EBV-EA(±) |
EBNA(+) |
7 |
M |
21 |
Chorea movement, hepatosplenomegaly, severe oral ulcer, history of pneumonia, thrombocytopenia, NK lymphocytosis |
2YA |
Liver, BM |
Present |
None |
29 (initial), 29-73.5 |
Positive |
EB-VCA, IgG(+) |
CD3+ |
Polyclonal (KIR: NK cells with clonality) |
CHOP |
10 mo |
Alive (improved) |
EB-VCA, IgM(–) |
CD4>CD8 |
ICE |
EBV-EA(–) |
CD56+ |
|
EBNA(+) |
|
|
8 |
F |
29 |
Fever, dizziness, nausea, hepatosplenomegaly, pancytopenia, LFT abnormality, diffuse lung infiltration |
2WA |
LN, lung, BM |
Absent |
None |
189.2 (initial), 189.2-1,897 |
Positive |
EB-VCA, IgG(+) |
CD3+ |
Monoclonal/polymorphic |
Self-limited |
6 mo |
Alive (persistent) |
EB-VCA, IgM(±) |
CD4+ |
EBV-EA(±) |
CD8– |
EBNA(+) |
CD56– |
9 |
M |
33 |
Fatigue, hepatosplenomegaly, NK lymphocytosis |
7MA |
Liver, BM |
Present |
None |
3,446 (initial), 1,918.6-12,112 |
Positive |
NA |
CD3+ |
NA |
Refuse |
8 mo |
Dead |
CD4<CD8 |
CD56– |
10 |
F |
41 |
Fever, hepatomegaly, abdominal pain, cerebral infact |
2YA |
BM |
Present |
Medium/ mild atypia |
1,231.8 (initial), 1,231.8-16,188 |
Positive |
NA |
CD3+ |
Polyclonal/polymorphic |
HLH-94a
|
30 mo |
Dead |
CD4– |
CVP |
CD8+ |
|
CD56– |
|
11 |
M |
44 |
LFT abnormality, hepatosplenomegaly, palpable neck mass |
8MA |
LN, liver |
Absent |
None |
NA |
Positive |
EB-VCA, IgG(+) |
CD3+ |
NA |
Refuse |
6 mo |
Dead |
EB-VCA, IgM(-) |
CD4+ |
EBV-EA(+) |
CD8+ |
EBNA(+) |
CD56– |
12 |
F |
59 |
Fever, myalgia, NK lymphocytosis |
7MA |
BM |
Present |
None |
65.28 (initial), 36.6-2,934 |
Negative |
NA |
CD3+ |
No band |
CVP, CHOP, IMVP-16/PD, VP |
4 mo |
Dead |
CD4– |
CD8+ |
CD56+ |